Management of paediatric ocular adnexal lymphoma by tumour location, histological subtype and stage
| No. (%)* | |||||||||
| Total* | S only | R only | C only | S+R | S+C | R+C | S+R+C | No treatment/ Unknown | |
| Conjunctival tumours | |||||||||
| DLBCL/Localised | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| FL/Localised | 1 (2) | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |
| EMZL/Localised | 20 (36) | 9 (45) | 1 (5) | 1 (5) | 7 (35) | 0 | 0 | 0 | 2 (10) |
| EMZL/Distant | 1 (2) | 0 | 0 | 0 | 1 | 0 | 0 | 0 | 0 |
| EMZL/Unknown | 1 (2) | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |
| Unknown/Localised | 2 (4) | 0 | 1 (50) | 0 | 0 | 1 (50) | 0 | 0 | 0 |
| Unknown/Unknown | 1 (2) | 1 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |
| Orbital tumours | |||||||||
| SLL/Localised | 1 (2) | 0 | 1 | 0 | 0 | 0 | 0 | 0 | 0 |
| DLBCL/Localised | 1 (2) | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
| DLBCL/Distant | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| DLBCL/Unknown | 1 (2) | 0 | 0 | 0 | 0 | 0 | 1 | 0 | 0 |
| DLBCLI/Localised | 1 (2) | 0 | 0 | 0 | 0 | 0 | 0 | 1 | 0 |
| BL/Distant | 2 (4) | 0 | 0 | 2 | 0 | 0 | 0 | 0 | 0 |
| EMZL/Localised | 2 (4) | 1 (50) | 0 | 0 | 1 (50) | 0 | 0 | 0 | 0 |
| EMZL/Distant | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| PTCL/Localised | 1 (2) | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
| ALCL/Regional | 1 (2) | 0 | 0 | 0 | 0 | 0 | 0 | 1 | 0 |
| ALCL/Distant | 1 (2) | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
| B-LBL/Localised | 2 (4) | 0 | 0 | 1 (50) | 0 | 1 (50) | 0 | 0 | 0 |
| B-LBL/Distant | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| Ph/Distant | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| Unknown/Localised | 3 (5) | 1 (33) | 0 | 0 | 0 | 1 (33) | 0 | 1 (33) | 0 |
| Unknown/Regional | 1 (2) | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
| Lacrimal tumours | |||||||||
| DLBCL/Unknown | 1 (2) | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 1 |
| BL/Localised | 1 (2) | 0 | 0 | 0 | 0 | 1 | 0 | 0 | 0 |
| FL/Localised | 1 (2) | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 1 |
| Unknown/Localised | 2 (4) | 1 (50) | 0 | 1 (50) | 0 | 0 | 0 | 0 | 0 |
| Eyelid tumours | |||||||||
| FL/Distant | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| Unknown/Localised | 1 (2) | 0 | 0 | 1 | 0 | 0 | 0 | 0 | 0 |
| Total* | 55 | 15 (27) | 3 (5) | 12 (22) | 9 (16) | 8 (15) | 1 (2) | 3 (5) | 4 (7) |
*Percentages were rounded up to integer numbers and may not add up to 100%.
.ALCL, anaplastic large T/null-cell lymphoma; BL, Burkitt lymphoma; B-LBL, lymphoblastic B-cell lymphoma; C, chemotherapy; DLBCL, diffuse large B-cell lymphoma; DLBCLI, diffuse large B-cell lymphoma, immunoblastic; EMZL, extranodal marginal zone lymphoma; FL, follicular lymphoma; Ph, lymphoma with Philadelphia translocation; PTCL, panniculitis-like T-cell lymphoma; R, radiation; S, surgery; SLL, small lymphocytic lymphoma.